EURORAD ESR

Case 8306

Congenital hepatic fibrosis

Author(s)
Battaglia V, Grigolini A, Gherarducci G, Calcagni F, Desideri I, Bartolozzi C
 
Patient
female, 39 year(s)
 
 
  • Figure 1
    Baseline CT examination

    Multiple cyst-like lesions all over the liver parenchyma.

     
    Area of Interest: Liver; Imaging Technique: CT;
     
     
  • Figure 2
    Conrast-enhanced portal phase CT
     

    MIP reconstruction shows a thin portal vein with no cavernomatosis.

     

    MIP reconstruction shows a thin portal vein with no cavernomatosis.

     

    Large pericolic and small perigastric venous collateral vessels.

     
     
     
  • Figure 3
    Contrast-enhanced arterial phase CT

    Pseudolesion (suspicion of fibrotic area, yellow circle), measuring approximately 25 mm, slightly hypervascular.

     
    Area of Interest: Liver; Imaging Technique: CT;
     
     
  • Figure 4
    Contrast-enhanced late phase CT

    The pseudolesion is isodense in late phase. A dot sign is not appreciable within the dilated bile ducts in segment VII.

     
    Area of Interest: Liver; Imaging Technique: CT;
     
     
  • Figure 5
    Baseline MR examination

    MR confirms the presence of the fibrotic area within segment II, which is slightly hyperintense on T1-w and slightly hypointense on T2-w. No fat is present within the fibrotic area.

     
     
     
  • Figure 6
    MRCP (T2-w MIP)

    Diffuse dilatation of the intrahepatic bile ducts in the rigth lobe, particularly at the level of the peripheral branches.

     
     
     
Multiple cyst-like lesions all over the liver parenchyma.
 
MIP reconstruction shows a thin portal vein with no cavernomatosis.
 
MIP reconstruction shows a thin portal vein with no cavernomatosis.
 
Large pericolic and small perigastric venous collateral vessels.
 
Pseudolesion (suspicion of fibrotic area, yellow circle), measuring approximately 25 mm, slightly hypervascular.
 
The pseudolesion is isodense in late phase. A dot sign is not appreciable within the dilated bile ducts in segment VII.
 
MR confirms the presence of the fibrotic area within segment II, which is slightly hyperintense on T1-w and slightly hypointense on T2-w. No fat is present within the fibrotic area.
 
Diffuse dilatation of the intrahepatic bile ducts in the rigth lobe, particularly at the level of the peripheral branches.
 
 
 
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