EURORAD ESR

Case 1394

ECR 2002 COD #12: Caroli's disease (type II) associated with medullary sponge kidney

Author(s)
Carlo Bartolozzi, MD
 
Patient
male, 23 year(s)
 
 
  • Figure 1
    Abdominal US
     

    Abdominal US examination shows multiple cystic lesions spread in both hepatic lobes. Within the cystic lesions internal tiny septa can be seen.

     
    Area of Interest: unknown; Imaging Technique: Abdominal US;

    US study demonstrates the presence of multiple microcysts and microstones located in the medulla of both kidneys.

     
    Area of Interest: unknown; Imaging Technique: Abdominal US;
     
     
  • Figure 2
    Upper abdominal CT
     

    Unenhanced CT scan confirms the presence of hepatic cystic lesions containing complete and incomplete septa.

     
    Area of Interest: unknown; Imaging Technique: Upper abdominal CT;

    Internal tiny septa within the cystic lesions don’t show contrast uptake at arterial phase CT scan.

     
    Area of Interest: unknown; Imaging Technique: Upper abdominal CT;

    Internal tiny septa within the cystic lesions show clear contrast uptake at portal-venous phase CT scan.

     
    Area of Interest: unknown; Imaging Technique: Upper abdominal CT;

    CT examination confirms multiple medullary microcysts and microstones in both kidneys.

     
    Area of Interest: unknown; Imaging Technique: Upper abdominal CT;
     
     
  • Figure 3
    MR cholangiography

    MR cholangiography with maximum-intensity projection reconstruction reveals cystic dilatations of the intrahepatic bile ducts communicating with the main bile duct. The insertion of the cystic duct into the main bile...

     
    Area of Interest: unknown; Imaging Technique: MR cholangiography;
     
     
  • Figure 4
    Gross pathology in a case of Caroli’s disease.

    Multiple cystic dilatations showing complete and incomplete bridging involve partially the biliary tree.

     
    Area of Interest: unknown; Imaging Technique: Gross pathology in a case of Caroli’s desease.;
     
     
  • Figure 5
    Histologic findings in a case of Caroli’s disease.

    Irregular dilatation of a bile duct (stars) with incomplete bridging of the ductal wall and a small portal branch (arrow) in the center of the bile duct are seen. Hepatic fibrosis is associated.

     
    Area of Interest: unknown; Imaging Technique: Histologic findings in a case of Caroli’s desease.;
     
     
Abdominal US examination shows multiple cystic lesions spread in both hepatic lobes. Within the cystic lesions internal tiny septa can be seen.
 
US study demonstrates the presence of multiple microcysts and microstones located in the medulla of both kidneys.
 
Unenhanced CT scan confirms the presence of hepatic cystic lesions containing complete and incomplete septa.
 
Internal tiny septa within the cystic lesions don’t show contrast uptake at arterial phase CT scan.
 
Internal tiny septa within the cystic lesions show clear contrast uptake at portal-venous phase CT scan.
 
CT examination confirms multiple medullary microcysts and microstones in both kidneys.
 
MR cholangiography with maximum-intensity projection reconstruction reveals cystic dilatations of the intrahepatic bile ducts communicating with the main bile duct. The insertion of the cystic duct into the main bile duct is located more inferior than typically seen.
 
Multiple cystic dilatations showing complete and incomplete bridging involve partially the biliary tree.
 
Irregular dilatation of a bile duct (stars) with incomplete bridging of the ductal wall and a small portal branch (arrow) in the center of the bile duct are seen. Hepatic fibrosis is associated.
 
 
 
Home Search Sections Teaching Cases History FAQ Case Archives Contact Login Disclaimer Imprint Switch to MOBILE version
View desktop version