EURORAD ESR

Case 13417

Erdheim-Chester disease

Author(s)
Leenknegt Benjamin, Dutoit Julie, Verstraete Koenraad

Department of Radiology,
Ghent University Hospital
 
Patient
male, 73 year(s)
 
 
  • Figure 1
    Osseous involvement
     

    Medullar osteosclerosis, cortical thickening and corticomedullar blurring of the left and right femur (upper figure, arrows). 18FDG-PET scanning reveals high FDG tracer uptake in the medulla of the left and right...

     
    Area of Interest: Bones; Extremities; Musculoskeletal bone; Imaging Technique: CT; PET; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;

    Medullar osteosclerosis of the left femur and tibia. Corresponding high FDG tracer uptake (arrows). Normal appearance of the epiphyses (left figure, arrowheads). Increased FDG tracer uptake in calcaneus, cuboid bone...

     
    Area of Interest: Bones; Extremities; Musculoskeletal bone; Imaging Technique: CT; PET; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;
     
     
  • Figure 2
    Thoracic and abdominal involvement
     

    Infiltration of the retrosternal soft tissues (thick arrow) and infiltration of the soft tissues around the thoracic aorta (thin arrow) with expansion into the left and right paravertebral space.

     
    Area of Interest: Arteries / Aorta; Thoracic wall; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;

    Infiltration of pleura posterior to the left ventricle (thick arrow) and of the soft tissues around the thoracic aorta (thin arrow) with expansion into the left and right paravertebral space.

     
    Area of Interest: Arteries / Aorta; Respiratory system; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;

    Soft tissue infiltration around the thoracic aorta (arrow) with expansion into the left and right paravertebral space.

     
    Area of Interest: Arteries / Aorta; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;

    Adrenal gland swelling with soft tissue infiltration of the adjacent fat and around the aorta (arrows). High FDG tracer uptake in the adrenals, around the aorta (arrows) and in the stomach (long arrow).

     
    Area of Interest: Adrenals; Arteries / Aorta; Stomach; Imaging Technique: CT; PET; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;

    Soft tissue infiltration of the left and right perirenal and posterior pararenal spaces (thin arrows). Infiltration of the left and right renal sinus (thick arrows). Infiltration around the abdominal aorta.

     
    Area of Interest: Arteries / Aorta; Kidney; Imaging Technique: CT; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;
     
     
  • Figure 3
    PET imaging
     

    Axial view of the brain shows a left-sided hypermetabolic spot anterior to the middle cerebral artery.

     
    Area of Interest: Neuroradiology brain; Imaging Technique: PET; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;

    Axial view of the feet shows a high FDG tracer uptake in the left and right calcaneus (upper figure, arrows), cuboid bone (middle figure, arrows) and metatarsals (lower figure, arrows).

     
    Area of Interest: Musculoskeletal bone; Imaging Technique: PET; Procedure: Diagnostic procedure; Special Focus: Connective tissue disorders;
     
     
Medullar osteosclerosis, cortical thickening and corticomedullar blurring of the left and right femur (upper figure, arrows). 18FDG-PET scanning reveals high FDG tracer uptake in the medulla of the left and right femur (lower figure, arrows).
 
Medullar osteosclerosis of the left femur and tibia. Corresponding high FDG tracer uptake (arrows). Normal appearance of the epiphyses (left figure, arrowheads). Increased FDG tracer uptake in calcaneus, cuboid bone and metatarsals (right figure, arrow).
 
Infiltration of the retrosternal soft tissues (thick arrow) and infiltration of the soft tissues around the thoracic aorta (thin arrow) with expansion into the left and right paravertebral space.
 
Infiltration of pleura posterior to the left ventricle (thick arrow) and of the soft tissues around the thoracic aorta (thin arrow) with expansion into the left and right paravertebral space.
 
Soft tissue infiltration around the thoracic aorta (arrow) with expansion into the left and right paravertebral space.
 
Adrenal gland swelling with soft tissue infiltration of the adjacent fat and around the aorta (arrows). High FDG tracer uptake in the adrenals, around the aorta (arrows) and in the stomach (long arrow).
 
Soft tissue infiltration of the left and right perirenal and posterior pararenal spaces (thin arrows). Infiltration of the left and right renal sinus (thick arrows). Infiltration around the abdominal aorta.
 
Axial view of the brain shows a left-sided hypermetabolic spot anterior to the middle cerebral artery.
 
Axial view of the feet shows a high FDG tracer uptake in the left and right calcaneus (upper figure, arrows), cuboid bone (middle figure, arrows) and metatarsals (lower figure, arrows).
 
 
 
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